Mediastinal lung herniation in an adult patient with Scimitar syndrome.

نویسندگان

  • Sait Demirkol
  • Ugur Bozlar
  • Sevket Balta
  • Murat Unlu
  • Turgay Celik
چکیده

Early cardiac abnormalities in obese children: importance of obesity per se versus associated cardiovascular risk factors. Delle Donne MG et al. Obesity cardiomyopathy: is it a reality? An ultrasonic tissue characterization study. Abnormal myocardial deformation properties in obese, non-hypertensive children : an ambulatory blood pressure monitoring, standard echocardiographic, and strain rate imaging study.tions of left ventricular myocardial characteristics associated with obesity. regional myocardial function quantification by two-dimensional strain: application in hypertrophic cardiomyopathy. Kisrieva-Ware Z et al. Effect of obesity and insulin resistance on myocardial substrate metabolism and efficiency in young women. Multiple markers of inflammation and weight status: cross-sectional analyses throughout childhood.toxic heart disease in obese rats: implications for human obesity. Effects of weight loss after gastric bypass on right and left ventricular function assessed by tissue Doppler imaging. A 26-year-old man was referred to our outpatient clinic with dyspnoea on exertion. He had a history of bronchial asthma and smoking. Chest X-ray was unremarkable. Transthoracic echocardiography showed slightly dilated right-sided cardiac chambers. We performed two-dimensional transeso-phageal echocardiography (2D TEE) and computed tomography (CT). 2D TEE showed that inferior vena cava (IVC) was larger than normal (Panel A and Supplementary data online, Video S1A). Coronal maximum intensity projection CT angiography image revealed anomalous drainage of a right pulmonary vein into the suprahepatic IVC (Panel B). Short-axis CT image revealed enlarged right ventricle (Panel C). Axial CT image demonstrated that medial segment of the right middle lobe lung protruded towards the left side behind the heart (Panel D, asterisk) and its pulmonary vein drained into the left lower pulmonary vein (Panel E, white arrow). Anterior segment of the left upper lobe lung drained directly the left atrium (Panel E, black arrow). The scimitar syndrome is characterized by partial or complete anomalous pulmonary venous connection of right lung into to the IVC. Mediastinal lung herniation should be differentiated from horseshoe lung. Mediastinal lung herniation may protrude to the opposite side while horseshoe lung is characterized by fusion of the posterobasal segment of the right and left lungs. The pulmonary-to-systemic blood flow ratio was 1.3, thus surgery was not performed. To the best of our knowledge, there are no reports in the literature on mediastinal lung herniation associated with Scimitar syndrome. Multimodality imaging can establish the diagnosis and enable a correct description of this anomaly. RV, right ventricle; IVC, inferior vena cava; LA, left atrium. Supplementary data are available at European Heart Journal …

برای دانلود رایگان متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Horseshoe lung associated with diaphragmatic herniation of the liver.

Horseshoe lung is a rare congenital pulmonary anomaly in which the caudal and basal segments of the left and right lungs are joined together behind the pericardium at the height of cardiac apex. Most patients with horseshoe lung have many other cardiovascular anomalies typical of the scimitar syndrome or the hypogenetic right lung syndrome. We report on a patient with horseshoe lung not associa...

متن کامل

Mediastinal Neuroendocrine Carcinoma of Unknown Origin Presenting with Superior Vena Cava Syndrome (SVCS): A Case Report

Primary neuroendocrine carcinoma (NEC) of the mediastinum is a rare type of carcinoma. According to the literature, only five cases of this condition have been reported so far. In this paper, we present a rare case of mediastinal NEC of unknown primary site. The patient was a 34-year-old man with mediastinal NEC, who presented with chronic dry cough and a right-sided mediastinal mass one year p...

متن کامل

Cushing’s syndrome associated with typical, peripheral pulmonary carcinoid tumor and N2 lymph node metastasis: case report

Background: The bronchopulmonary carcinoid tumor accounts for 1-2% of all adult malignancies of the lung and 20-30% of all carcinoid tumors. Cushing’s syndrome is the result of chronic exposure to increased concentration of exogenous or endo-genus cortisol hormone, and it is generally associated with central obesity, metabolic syndrome, and hypertension. Treatment is based on decreasing cortiso...

متن کامل

A case report of variant scimitar syndrome

Background: Scimitar syndrome (SS) or congenital pulmonary venolobar syndrome is a rare anomaly, most commonly including partial pulmonary venous drainage into the inferior vena cava, right lung hypoplasia, dextroposition of the heart, and anomalous systemic arterial supply from aorta or one of its branches to the right lung. Case report: A 10-day-old female infant was referred to our hospital...

متن کامل

Scimitar Syndrome: Pathology, Clinical Presentation, Radiographic Features, and Treatment

Scimitar syndrome is characterized by partial or total anomalous pulmonary venous return from the right lung along with pulmonary hypoplasia.Wesearched the mail databases such as Medline (via PubMed), Scopus and EMBASE and Google Scholar. Diagnosing infantile scimitar syndrome requires meticulous attention and high suspicion of the early referral and management. The association of the syndrome ...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

عنوان ژورنال:
  • European heart journal cardiovascular Imaging

دوره 14 7  شماره 

صفحات  -

تاریخ انتشار 2013